Blue Rubber Nevus Syndrome Treatments

Introduction blue rubber bleb nevus syndrome brbns also known as bean s syndrome is an atypical type of vascular malformation.

Blue rubber nevus syndrome treatments.

Blue rubber bleb nevus syndrome is a condition in which the blood vessels do not develop properly in an area of the skin or other body organ particularly the intestines. Blue rubber bleb nevus syndrome brbns is a rare blood vessel vascular disorder that affects the skin and internal organs of the body. However it was later made famous in 1958 by william bennett bean for which the disease has been termed bean syndrome later referenced as. What is blue rubber bleb nevus syndrome.

Blue rubber bleb nevus syndrome brbns sometimes called bean syndrome is a rare congenital vascular anomaly in which malformed veins or blebs appear on the skin and surfaces of internal organs. This condition was initially discovered in 1860 by gascoyen. Multiple distinctive skin lesions are usually characteristic of this disorder and are often present at birth or present during early childhood. These small purple lesions are particularly common in the gastrointestinal gi tract.

Given the clinical and imagiological features we established the diagnosis of a sporadic type of blue rubber bleb nevus syndrome brbns. Blue rubber bleb nevus syndrome brbns is a rare condition that is characterized by numerous malformations of the venous system that significantly involve the skin and visceral organs. This condition was initially discovered in 1860 by gascoyen. Blue rubber bleb nevus syndrome brbns is a rare condition that is characterized by numerous malformations of the venous system that significantly involve the skin and visceral organs.

The disease is characterized by the presence of fluid filled blisters as visible circumscribed chronic lesions nevus it was described by william bean in 1958. The malformed blood vessels appear as a spot or lesion called a nevus. Formerly called as gascoyen syndrome blue rubber bleb nevus syndrome also known as bean syndrome is an uncommon hereditary disease referring to the abnormality in the blood vessels particularly in the small intestine and distal large bowel of the digestive system in addition to multiple venous malformations involving most prominently the skin and. The underlying blood vessel malformations are present from birth even though the nevus may not be visible until later in life.